[1]朱峰,陈铀.先天性心脏病相关肺动脉高压的治疗进展[J].心血管病学进展,2019,(6):894-897.[doi:10.16806/j.cnki.issn.1004-3934.2019.06.014]
 ZHU Feng,CHEN You.Congenital Heart Disease-related Pulmonary Arterial Hypertension[J].Advances in Cardiovascular Diseases,2019,(6):894-897.[doi:10.16806/j.cnki.issn.1004-3934.2019.06.014]
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先天性心脏病相关肺动脉高压的治疗进展()
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《心血管病学进展》[ISSN:51-1187/R/CN:1004-3934]

卷:
期数:
2019年6期
页码:
894-897
栏目:
综述
出版日期:
2019-09-25

文章信息/Info

Title:
Congenital Heart Disease-related Pulmonary Arterial Hypertension
作者:
朱峰1 陈铀2
(新疆医科大学第一附属医院,新疆 乌鲁木齐 830054;2.新疆医科大学第一附属医院心内科,新疆 乌鲁木齐 830054)
Author(s):
ZHU Feng1 CHEN You2
(The First Affiliated Hospital of Xinjiang Medical University, Urumqi 830054,Xinjiang,China; 2.Department of Cardiology, The First Affiliated Hospital of Xinjiang Medical University, Urumqi 830054,Xinjiang,China)
关键词:
先天性心脏病 肺动脉高压 药物治疗 进展
Keywords:
Congenital heart diseasePulmonary arterial hypertensionMedication treatmentProgress
DOI:
10.16806/j.cnki.issn.1004-3934.2019.06.014
摘要:
先天性心脏病是中国常见出生缺陷,由先天性心脏病引起的肺动脉高压在中国占重要的地位,是影响先天性心脏病治疗效果和预后的重要因素。该类患者发现时多为晚期,预后极差,靶向药物的不断更新和介入手术的完善使预后有了新的希望。现就先天性心脏病相关肺动脉高压的药物治疗、介入治疗及外科治疗相关进展进行综述,以期为进一步研究提供依据。
Abstract:
Congenital heart disease is a common birth defect in China. Pulmonary arterial hypertension caused by congenital heart disease plays an important role in China and it is an important factor affecting the therapeutic effect and prognosis of congenital heart disease. Most of these patient were found in late stage,and the prognosis is very poor.The continuous updating of targeted drugs and the improvement of interventional surgery have given new hope to the prognosis. The progress of drug therapy, interventional therapy and surgical treatment of congenital heart disease-related pulmonary arterial hypertension is reviewed to provide a basis for further research.

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备注/Memo

备注/Memo:
基金项目:国家自然科学基金项目(81860064)
通信作者:陈铀, E-mail?donny666@sina.com
更新日期/Last Update: 2019-12-13