[1]杜楚豪 董捷 董硕 徐海涛 孙阳雪 李守军 杨克明 闫军.Fontan循环的新时代-远期淋巴系统并发症研究进展[J].心血管病学进展,2024,(4):299.[doi:10.16806/j.cnki.issn.1004-3934.2024.02.003]
 DU Chuhao,DONG Jie,DONG Shuo,et al.New Era of Fontan CirculationResearch Progress in Long Term Lymphatic System Complications[J].Advances in Cardiovascular Diseases,2024,(4):299.[doi:10.16806/j.cnki.issn.1004-3934.2024.02.003]
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Fontan循环的新时代-远期淋巴系统并发症研究进展()
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《心血管病学进展》[ISSN:51-1187/R/CN:1004-3934]

卷:
期数:
2024年4期
页码:
299
栏目:
综述
出版日期:
2024-04-25

文章信息/Info

Title:
New Era of Fontan CirculationResearch Progress in Long Term Lymphatic System Complications
作者:
杜楚豪 董捷 董硕 徐海涛 孙阳雪 李守军 杨克明 闫军
(中国医学科学院 北京协和医学院 国家心血管病中心 阜外医院小儿外科中心,北京 100037)
Author(s):
DU ChuhaoDONG JieDONG ShuoLIU ShunXU HaitaoSUN YangxueLI ShoujunYANG KemingYAN Jun
(Department of Pediatric Cardiac Surgery, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing 100037, China)
关键词:
Fontan循环淋巴系统并发症塑型性支气管炎蛋白丢失性肠病淋巴管介入治疗
Keywords:
Fontan circulation Lymphatic system complications Plastic bronchitis Protein loss enteropathy Lymphatic interventional therapy
DOI:
10.16806/j.cnki.issn.1004-3934.2024.02.003
摘要:
全腔静脉-肺动脉连接术(Fontan姑息手术)挽救了大量单心室结构患儿的生命。然而,术后远期淋巴系统并发症严重影响着患者的预后。回顾既往相关文献,总结Fontan患者淋巴系统并发症的自然病程、病理生理、临床表现、诊断和治疗管理。
Abstract:
Total cavopulmonary connection (Fontan procedure) has saved the lives of a large number of children with single ventricle, in which a biventricular repair is not possible. However, postoperative long-term lymphatic complications seriously affect the prognosis of patients. This article reviews the previous literature and summarizes the natural history, pathophysiology, clinical manifestations, diagnosis, and management of lymphatic complications in patients with Fontan circulation

参考文献/References:

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备注/Memo

备注/Memo:
收稿日期:2023-05-14
更新日期/Last Update: 2024-05-31