[1]聂晓宇 钱来军 刘晓龙 任雨萌 胡志耕.心尖部肥厚型心肌病的病理生理和心电图特点[J].心血管病学进展,2025,(5):399.[doi:10.16806/j.cnki.issn.1004-3934.2025.05.004]
　NIE Xiaoyu,QIAN Laijun,LIU Xiaolong,et al.Pathophysiological and Electrocardiographic Characteristics of Apical Hypertrophic Cardiomyopathy?/html>[J].Advances in Cardiovascular Diseases,2025,(5):399.[doi:10.16806/j.cnki.issn.1004-3934.2025.05.004]
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心尖部肥厚型心肌病的病理生理和心电图特点()

《心血管病学进展》[ISSN:51-1187/R/CN:1004-3934]

卷:
期数:
2025年5期
页码:
399
栏目:
综述
出版日期:
2025-05-25

文章信息/Info

Title:
Pathophysiological and Electrocardiographic Characteristics of Apical Hypertrophic Cardiomyopathy?/html>
作者:
聂晓宇 钱来军 刘晓龙 任雨萌 胡志耕
(山西中医药大学附属医院心内科,山西 太原 030000)
Author(s):
NIE Xiaoyu; QIAN Laijun; LIU Xiaolong; REN Yumeng; HU Zhigeng
(Department of Cardiology,Affiliated Hospital of Shanxi University of Traditional Chinese Medicine,Taiyuan 030000,Shanxi,China)
关键词:
心尖部肥厚型心肌病; 病理生理; 心电图
Keywords:
Apical hypertrophic cardiomyopathy; Pathophysiology;  Electrocardiogram
DOI:
10.16806/j.cnki.issn.1004-3934.2025.05.004
摘要:
心尖部肥厚型心肌病（APH）是一种常染色体遗传性心肌病，以左心室心尖部肥厚为解剖特点，与经典肥厚型心肌病相比，APH更加散发，临床特点不明显，患者常以胸闷、胸痛、呼吸困难为首诊，再结合其心电图表现，极易误诊为急性冠脉综合征，如不能早期识别，多发生低血压、晕厥、栓塞、心房颤动等恶性临床事件。因此了解及掌握APH的特点及心电图特征有助于更快地识别并开展临床诊治工作。
Abstract:
Apical hypertrophic cardiomyopathy(APH) is an autosomal hereditary cardiomyopathy,characterized anatomically by hypertrophy of the apical portion of the left ventricle. Compared with classical hypertrophic cardiomyopathy,APH is more disseminated and has less obvious clinical features. Patients are often diagnosed with chest tightness,chest pain,and dyspnea as the first diagnosis,and then combined with their electrocardiogram,it is easy to misdiagnose them as acute coronary syndromes. If they are not recognized at an early stage,malignant clinical events such as hypotension,syncope,embolism and atrial fibrillation occur. Therefore,understanding and mastering the characteristics of APH and electrocardiogram features can help identify and carry out clinical diagnosis and treatment work more quickly.

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更新日期/Last Update: 2025-06-26